| Peer-Reviewed

Extra Anatomic Repair of Interrupted Aortic Arch

Received: 25 September 2019     Accepted: 16 October 2019     Published: 4 November 2019
Views:       Downloads:
Abstract

Interrupted Aortic Arch is a rare congenital anomaly with an incidence of 2 per 100,000 live births. It is almost always (95-97%) associated with structural abnormality like VSD. Interrupted Aortic Arch is usually diagnosed soon after birth, and when left untreated results in 90% mortality at a median age of 4 days. Isolated IAA is a very rare entity. Substantial collateral circulation must be present to maintain flow and enable survival. Conventional surgical repair is a challenge due to extensive collateral circulation in patients who have survived to adulthood. Here, we report a patient with an isolated IAA without any associated defect who survived into third decade. The patient presented with complaints of palpitations, uncontrolled hypertension, and weakness in lower limbs and on evaluation, he had isolated Interrupted Aortic Arch. We managed to do an Extra anatomical Bypass graft from ascending aorta to descending aorta on a beating heart with minimal risk. The procedure was done through median sternotomy to avoid the damage to collaterals when approached through thoracotomy.

Published in International Journal of Cardiovascular and Thoracic Surgery (Volume 5, Issue 5)
DOI 10.11648/j.ijcts.20190505.11
Page(s) 72-75
Creative Commons

This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.

Copyright

Copyright © The Author(s), 2019. Published by Science Publishing Group

Keywords

Interrupted Aortic Arch, Extra Anatomical Bypass, Sternotomy, Collaterals, IAA

References
[1] Steidele RJ. Samml Chir u Med Beob (Vienna) 1778; 2: 114.
[2] Messner G, Reul GJ, Flamm SD, et al. Interrupted Aortic Arch in an Adult: Single-Stage Extra-Anatomic Repair. Tex Heart Inst J 2002; 29: 118-21.
[3] Celoria GC, Patton RB. Congenital absence of aortic arch. Am Heart J 1959; 58: 407-13.
[4] Jacobs ML, Chin AJ, Rychik J. et al. Interrupted Aortic Arch: Impact of Subaortic Stenosis on Management and Outcome. Circulation 1995; 92: 128-31.
[5] Said, Sameh M.; Burkhart, Harold M.; Dearani, Joseph A.; Connolly, Heidi M.; Schaff, Hartzell V. Ascending-to-descending aortic bypass: A simple solution to a complex problem. In: Annals of Thoracic Surgery. 2014; Vol. 97, No. 6. pp. 2041-2048.
[6] Prasad SV, Gupta SK, Reddy KN, Murthy JS, Gupta SR, Somnath HS. Isolated interrupted aortic arch in adult. Indian Heart J 1988; 40: 108-12.
[7] Clarence S. Weldon, M. D., Alexis F. Hartmann, Jr., M. D., Neil G. Steinhoff, M. D., and James D. Morrissey, M. D. A Simple, Safe, and Rapid Technique for the Management of Recurrent Coarctation of the Aorta.
[8] Siderys H, Graffis R, Halbrook H, Kasbeckar V. A technique for management of inaccessible coarctation of the aorta. J Thorac Cardiovasc Surg 1974; 67: 568-70.
[9] Wukasch DC, Cooley DA, Sandiford FM, Nappi G, Reul GJ Jr. Ascending aorta–abdominal aorta bypass: indications, technique, and report of 12 patients. Ann Thorac Surg 1977; 23: 442-8.
[10] Edie RN, Janani J, Attai LA, Malm JR, Robinson G. Bypass grafts for recurrent or complex coarctations of the aorta. Ann Thorac Surg 1975; 20: 558-66.
[11] Vijayanagar R, Natarajan P, Eckstein PF, Bognolo DA, Toole JC. Aortic valvular insufficiency and postductal aortic coarctation in the adult: combined surgical management through median sternotomy—a new surgical approach. J Thorac Cardiovasc Surg 1980; 79: 266-8.
[12] Akl BF. Ascending-distal aorta bypass [letter]. Ann Thorac Surg 1985; 39: 196.
[13] Karolczak MA, McKay R, Arnold R. Right-sided intrathoracic bypass graft for complex or recurrent coarctation of the aorta. Eur J Cardiothorac Surg 1989: 3; 278-81.
[14] Fokin A, Orechowa L, Werbowetsky L. Aorto-aortic bypass through the right pleural cavity in recurrent coarctation of the aorta. Vasa 1992; 21: 422-3.
[15] Caspi J, Ilbawi MN, Milo S, Bar-El Y, Roberson DA, Thilenius OG, et al. Alternative techniques for surgical management of recoarctation. Eur J Cardiothorac Surg 1997; 12: 116-9.
[16] Iguro Y, Yamashita M, Murata R, Fukumoto Y, Taira A. Rightsided intrathoracic bypass grafting for a coarctation of the aorta in an advanced aged woman. J Jpn Assoc Thorac Surg 1997; 45: 1743-6.
[17] Heinemann MK, Ziemer G, Wahlers T, Köhler A, Borst HG. Extraanatomic thoracic aortic bypass grafts: indications, techniques, and results. Eur J Cardiothorac Surg 1997; 11: 169-75.
[18] Brown J. W., Ruzmetov M., Okada Y., Vijay P., Rodefeld M. D., Turrentine M. W.. Outcomes in patients with interrupted aortic arch and associated anomalies: a 20-year experience, Eur J Cardiothorac Surg, 2006, vol. 29 5 (pg. 666-673).
[19] Serraf A., Lacour-Gayet F., Robotin M., Bruniaux J., Sousa-Uva M., Roussin R., Planché C.. Repair of interrupted aortic arch: a ten-year experience, J Thorac Cardiovasc Surg, 1996, vol. 112 November (5) (pg. 1150-1160).
[20] Sell J. E., Jonas R. A., Mayer J. E., Blackstone E. H., Kirklin J. W., Castaneda A. R.. The results of a surgical program for interrupted aortic arch, J Thorac Cardiovasc Surg, 1988, vol. 96 December (6) (pg. 864-877).
[21] Karl T. R., Sano S., Brawn W., Mee R. B.. Repair of hypoplastic or interrupted aortic arch via sternotomy, J Thorac Cardiovasc Surg, 1992, vol. 104 (pg. 688-695).
[22] Mainwaring R. D., Lamberti J. J.. Mid- to long-term results of the two-stage approach for type B interrupted aortic arch and ventricular septal defect, Ann Thorac Surg, 1997, vol. 64 (pg. 1782-1786).
[23] Vouhé P. R., Macé L., Vernant F., Jayais P., Pouard P., Mauriat P., Leca F., Neveux J. Y.. Primary definitive repair of interrupted aortic arch with ventricular septal defect, Eur J Cardiothorac Surg, 1990, vol. 4 (pg. 365-370).
[24] Tláskal T., Hucín B., Hruda J., Marek J., Chaloupecký V., Kostelka M., Janousek J., Skovránek J.. Results of primary and two-stage repair of interrupted aortic arch, Eur J Cardiothorac Surg, 1998, vol. 14 September (3) (pg. 235-242).
[25] McCrindle B. W., Tchervenkov C. I., Konstantinov I. E., Williams W. G., Neirotti R. A., Jacobs M. L., Blackstone E. H., Congenital Heart Surgeons Society. Risk factors associated with mortality and interventions in 472 neonates with interrupted aortic arch: a Congenital Heart Surgeons Society study, J Thorac Cardiovasc Surg, 2005, vol. 129 February (2) (pg. 343-350).
[26] Tchervenkov C. I., Tahta S. A., Jutras L., Béland M. J.. Single-stage repair of aortic arch obstruction and associated intracardiac defects with pulmonary homograft patch aortoplasty, J Thorac Cardiovasc Surg, 1998, vol. 116 December (6) (pg. 897-904).
[27] Leoni F., Huhta J. C., Douglas J., MacKay R., de Leval M. R., Macartney F. J., Stark J.. Effect of prostaglandin on early surgical mortality in obstructive lesions of the systemic circulation, Br Heart J, 1984, vol. 52 (pg. 654-659).
[28] Luciani G. B., Ackerman R. J., Chang A. C., Wells W. J., Starnes V. A.. One-stage repair of interrupted aortic arch, ventricular septal defect, and subaortic obstruction in the neonate: a novel approach, J Thorac Cardiovasc Surg, 1996, vol. 111 (pg. 48-358).
Cite This Article
  • APA Style

    Anirudh Kumar Paidi, Palli Venkata Naresh Kumar, Madhava Rao Midhe, Ravi Kiran Mamidala, Venkat Reddy Navuluri. (2019). Extra Anatomic Repair of Interrupted Aortic Arch. International Journal of Cardiovascular and Thoracic Surgery, 5(5), 72-75. https://doi.org/10.11648/j.ijcts.20190505.11

    Copy | Download

    ACS Style

    Anirudh Kumar Paidi; Palli Venkata Naresh Kumar; Madhava Rao Midhe; Ravi Kiran Mamidala; Venkat Reddy Navuluri. Extra Anatomic Repair of Interrupted Aortic Arch. Int. J. Cardiovasc. Thorac. Surg. 2019, 5(5), 72-75. doi: 10.11648/j.ijcts.20190505.11

    Copy | Download

    AMA Style

    Anirudh Kumar Paidi, Palli Venkata Naresh Kumar, Madhava Rao Midhe, Ravi Kiran Mamidala, Venkat Reddy Navuluri. Extra Anatomic Repair of Interrupted Aortic Arch. Int J Cardiovasc Thorac Surg. 2019;5(5):72-75. doi: 10.11648/j.ijcts.20190505.11

    Copy | Download

  • @article{10.11648/j.ijcts.20190505.11,
      author = {Anirudh Kumar Paidi and Palli Venkata Naresh Kumar and Madhava Rao Midhe and Ravi Kiran Mamidala and Venkat Reddy Navuluri},
      title = {Extra Anatomic Repair of Interrupted Aortic Arch},
      journal = {International Journal of Cardiovascular and Thoracic Surgery},
      volume = {5},
      number = {5},
      pages = {72-75},
      doi = {10.11648/j.ijcts.20190505.11},
      url = {https://doi.org/10.11648/j.ijcts.20190505.11},
      eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ijcts.20190505.11},
      abstract = {Interrupted Aortic Arch is a rare congenital anomaly with an incidence of 2 per 100,000 live births. It is almost always (95-97%) associated with structural abnormality like VSD. Interrupted Aortic Arch is usually diagnosed soon after birth, and when left untreated results in 90% mortality at a median age of 4 days. Isolated IAA is a very rare entity. Substantial collateral circulation must be present to maintain flow and enable survival. Conventional surgical repair is a challenge due to extensive collateral circulation in patients who have survived to adulthood. Here, we report a patient with an isolated IAA without any associated defect who survived into third decade. The patient presented with complaints of palpitations, uncontrolled hypertension, and weakness in lower limbs and on evaluation, he had isolated Interrupted Aortic Arch. We managed to do an Extra anatomical Bypass graft from ascending aorta to descending aorta on a beating heart with minimal risk. The procedure was done through median sternotomy to avoid the damage to collaterals when approached through thoracotomy.},
     year = {2019}
    }
    

    Copy | Download

  • TY  - JOUR
    T1  - Extra Anatomic Repair of Interrupted Aortic Arch
    AU  - Anirudh Kumar Paidi
    AU  - Palli Venkata Naresh Kumar
    AU  - Madhava Rao Midhe
    AU  - Ravi Kiran Mamidala
    AU  - Venkat Reddy Navuluri
    Y1  - 2019/11/04
    PY  - 2019
    N1  - https://doi.org/10.11648/j.ijcts.20190505.11
    DO  - 10.11648/j.ijcts.20190505.11
    T2  - International Journal of Cardiovascular and Thoracic Surgery
    JF  - International Journal of Cardiovascular and Thoracic Surgery
    JO  - International Journal of Cardiovascular and Thoracic Surgery
    SP  - 72
    EP  - 75
    PB  - Science Publishing Group
    SN  - 2575-4882
    UR  - https://doi.org/10.11648/j.ijcts.20190505.11
    AB  - Interrupted Aortic Arch is a rare congenital anomaly with an incidence of 2 per 100,000 live births. It is almost always (95-97%) associated with structural abnormality like VSD. Interrupted Aortic Arch is usually diagnosed soon after birth, and when left untreated results in 90% mortality at a median age of 4 days. Isolated IAA is a very rare entity. Substantial collateral circulation must be present to maintain flow and enable survival. Conventional surgical repair is a challenge due to extensive collateral circulation in patients who have survived to adulthood. Here, we report a patient with an isolated IAA without any associated defect who survived into third decade. The patient presented with complaints of palpitations, uncontrolled hypertension, and weakness in lower limbs and on evaluation, he had isolated Interrupted Aortic Arch. We managed to do an Extra anatomical Bypass graft from ascending aorta to descending aorta on a beating heart with minimal risk. The procedure was done through median sternotomy to avoid the damage to collaterals when approached through thoracotomy.
    VL  - 5
    IS  - 5
    ER  - 

    Copy | Download

Author Information
  • Department of Cardiovascular and Thoracic Surgery, Yashoda Hospitals, Hyderabad, India

  • Department of Cardiovascular and Thoracic Surgery, Yashoda Hospitals, Hyderabad, India

  • Department of Cardiac Anaesthesia, Yashoda Hospitals, Hyderabad, India

  • Department of Cardiovascular and Thoracic Surgery, Yashoda Hospitals, Hyderabad, India

  • Department of Perfusion, Yashoda Hospitals, Hyderabad, India

  • Sections