| Peer-Reviewed

A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve

Received: 25 December 2022     Accepted: 27 January 2023     Published: 9 February 2023
Views:       Downloads:
Abstract

Background: Truncus arteriosus is a rare congenital heart malformation requiring repair in the neonatal period. Without correction, the majority of patients die within the first year of life. However, this case shows that some patients remain operable even at an advanced age. Case presentation: We report the case of an 8-year-old girl with type 2 truncus arteriosus with pulmonary vascular protection by a particular opening of the truncal valve partially obstructing the origin of the pulmonary artery in systole and causing a reduction in pulmonary flow. The initial evaluation based on the clinical presentation, the electrocardiogram and the echocardiography showed a significant elevation of the pressures of the right ventricle with a functional stenosis at the origin of the pulmonary artery. Hemodynamic exploration demonstrated that the pulmonary arterial hypertension is reversible, thereby the patient was successfully operated. Conclusion: The objective of this observation is to demonstrate that truncus arteriosus referred late does not eliminate the possibility of complete surgical repair, which underlines the importance of an exhaustive evaluation of these patients based on several arguments.

Published in International Journal of Cardiovascular and Thoracic Surgery (Volume 8, Issue 6)
DOI 10.11648/j.ijcts.20220806.11
Page(s) 59-62
Creative Commons

This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.

Copyright

Copyright © The Author(s), 2023. Published by Science Publishing Group

Keywords

Congenital Heart Defect, Truncus Arteriosus, Pulmonary Hypertension

References
[1] Keith JD, Rowe RD, Vlad P, editors. Heart disease in infancy and childhood. New York: Macmillan Prevalence, incidence and epidemiology; 1978. p. 3–13. (1 talwa).
[2] Yoshizato T, Julsrud PR. Truncus arteriosus revisited: an angiographic demonstration. Pediatr Cardiol 1990; 11: 36–40.
[3] Kharwar RB, et al. Persistent truncus arteriosus: a rare survival beyond the first decade. J Am Coll Cardiol. 2014; 63 (17): 1807. doi: 10.1016/j.jacc.2013.12.054. [PubMed] [CrossRef] [Google Scholar].
[4] Abid D, et al. Unrepaired persistent truncus arteriosus in a 38-year-old woman with an uneventful pregnancy. Cardiovasc J Afr. 2015; 26 (4): e6–8. doi: 10.5830/CVJA-2015-005. [PMC free article] [PubMed] [CrossRef] [Google Scholar].
[5] Urban AE, Sinzobahamvya N, Brecher AM, Wetter J, Malorny S. Truncus arteriosus: ten-year experience with homograft repair in neonates and infants. Ann Thorac Surg 1998; 66: S183–8.
[6] Sachin Talwar et al. Persistent truncus arteriosus repaired beyond infancyIndian J Thorac Cardiovasc Surg (July–September 2012) 28 (3): 171–176.
[7] Marcelletti C, et al. Early and late results of surgical repair of truncus arteriosus. Circulation. 1977; 55 (4): 636–41. doi: 10.1161/01.CIR.55.4.636. [PubMed] [CrossRef] [Google Scholar.
[8] Viswanathan S, Kumar RK. Assessment of operability of congenital cardiac shunts with increased pulmonary vascular resistance. Catheter Cardiovasc Interv 2008; 71: 665–670. 10.1002/ccd.21446.
[9] M Gouton et al. Late management of truncus arteriosus: 20 years of humanitarian experience Cardiol Young. Feb. 2018 Feb; 28 (2): 302-308.
[10] Qiuming Chen, and al, Outcomes of Surgical Repair for Persistent Truncus Arteriosus from Neonates to Adults: A Single Center's Experience, PLoS One. 2016; 11 (1): e0146800.
[11] Chen SJ, Huang JH, Lee WJ, Lin MT, Chen YS, Wang JK. Diagnosis of pulmonary arterial hypertension in children by using cardiac computed tomography. Korean J Radiol. (2019) 20: 976–84.
[12] Caro-Domínguez P, Compton G, Humpl T, Manson DE. Pulmonary arterial hypertension in children: diagnosis using ratio of main pulmonary artery to ascending aorta diameter as determined by multi-detector computed tomography. Pediatr Radiol. (2016) 46: 1378–83. doi: 10.1007/s00247-016-3636-5.
[13] Zhu Y, Jiang Q, Zhang W, Hu R, Dong W, Zhang H and Zhang H (2022) Outcomes and occurrence of post-operative pulmonary hypertension crisis after late referral truncus arteriosus repair. Front. Cardiovasc. Med. 9: 999032.
[14] Talwar S, Choudhary SK, Garg S, et al. Unidirectional valved patch closure of ventricular septal defects with severe pulmonary arterial hypertension. Interactive Cardio Vasc Thorac Surg. 2012; 14: 699–703.
[15] Novick WM, Sandoval N, Lazorhysynets VV, et al Flap valve double patch closure of ventricular septal defects in children with increased pulmonary vascular resistance. Ann Thorac Surg. 2005; 79 (1): 21-28. 7.
[16] Perri G, Filippelli S, Polito A, Di Carlo D, Albanese SB, Carotti A. Repair of incompetent truncal valves: early and mid-term results. Interact Cardiovasc Thorac Surg 2013; 16: 808–813. 23.
[17] Karl TR. Safe surgical strategy for extracardiac conduit replacement in common arterial trunk. Cardiol Young 2012; 22: 708–717.
Cite This Article
  • APA Style

    Karima Hami, Rida Ajaja, Younes Cheikhaoui. (2023). A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve. International Journal of Cardiovascular and Thoracic Surgery, 8(6), 59-62. https://doi.org/10.11648/j.ijcts.20220806.11

    Copy | Download

    ACS Style

    Karima Hami; Rida Ajaja; Younes Cheikhaoui. A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve. Int. J. Cardiovasc. Thorac. Surg. 2023, 8(6), 59-62. doi: 10.11648/j.ijcts.20220806.11

    Copy | Download

    AMA Style

    Karima Hami, Rida Ajaja, Younes Cheikhaoui. A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve. Int J Cardiovasc Thorac Surg. 2023;8(6):59-62. doi: 10.11648/j.ijcts.20220806.11

    Copy | Download

  • @article{10.11648/j.ijcts.20220806.11,
      author = {Karima Hami and Rida Ajaja and Younes Cheikhaoui},
      title = {A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve},
      journal = {International Journal of Cardiovascular and Thoracic Surgery},
      volume = {8},
      number = {6},
      pages = {59-62},
      doi = {10.11648/j.ijcts.20220806.11},
      url = {https://doi.org/10.11648/j.ijcts.20220806.11},
      eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ijcts.20220806.11},
      abstract = {Background: Truncus arteriosus is a rare congenital heart malformation requiring repair in the neonatal period. Without correction, the majority of patients die within the first year of life. However, this case shows that some patients remain operable even at an advanced age. Case presentation: We report the case of an 8-year-old girl with type 2 truncus arteriosus with pulmonary vascular protection by a particular opening of the truncal valve partially obstructing the origin of the pulmonary artery in systole and causing a reduction in pulmonary flow. The initial evaluation based on the clinical presentation, the electrocardiogram and the echocardiography showed a significant elevation of the pressures of the right ventricle with a functional stenosis at the origin of the pulmonary artery. Hemodynamic exploration demonstrated that the pulmonary arterial hypertension is reversible, thereby the patient was successfully operated. Conclusion: The objective of this observation is to demonstrate that truncus arteriosus referred late does not eliminate the possibility of complete surgical repair, which underlines the importance of an exhaustive evaluation of these patients based on several arguments.},
     year = {2023}
    }
    

    Copy | Download

  • TY  - JOUR
    T1  - A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve
    AU  - Karima Hami
    AU  - Rida Ajaja
    AU  - Younes Cheikhaoui
    Y1  - 2023/02/09
    PY  - 2023
    N1  - https://doi.org/10.11648/j.ijcts.20220806.11
    DO  - 10.11648/j.ijcts.20220806.11
    T2  - International Journal of Cardiovascular and Thoracic Surgery
    JF  - International Journal of Cardiovascular and Thoracic Surgery
    JO  - International Journal of Cardiovascular and Thoracic Surgery
    SP  - 59
    EP  - 62
    PB  - Science Publishing Group
    SN  - 2575-4882
    UR  - https://doi.org/10.11648/j.ijcts.20220806.11
    AB  - Background: Truncus arteriosus is a rare congenital heart malformation requiring repair in the neonatal period. Without correction, the majority of patients die within the first year of life. However, this case shows that some patients remain operable even at an advanced age. Case presentation: We report the case of an 8-year-old girl with type 2 truncus arteriosus with pulmonary vascular protection by a particular opening of the truncal valve partially obstructing the origin of the pulmonary artery in systole and causing a reduction in pulmonary flow. The initial evaluation based on the clinical presentation, the electrocardiogram and the echocardiography showed a significant elevation of the pressures of the right ventricle with a functional stenosis at the origin of the pulmonary artery. Hemodynamic exploration demonstrated that the pulmonary arterial hypertension is reversible, thereby the patient was successfully operated. Conclusion: The objective of this observation is to demonstrate that truncus arteriosus referred late does not eliminate the possibility of complete surgical repair, which underlines the importance of an exhaustive evaluation of these patients based on several arguments.
    VL  - 8
    IS  - 6
    ER  - 

    Copy | Download

Author Information
  • Congenital Cardiology Unit, Cheikh Zaid Hospital, Abulcassis University, Rabat, Morocco

  • Congenital Cardiology Unit, Cheikh Zaid Hospital, Abulcassis University, Rabat, Morocco

  • Congenital Cardiology Unit, Cheikh Zaid Hospital, Abulcassis University, Rabat, Morocco

  • Sections